Nicolau syndrome with pemphigus vulgaris: a rare case report and review of literature

Future Journal of Pharmaceutical Sciences

Table 1 Pemphigus disease area index scores for 6 follow-ups

Follow-up	Disease activity scores				Disease damage scores			Total score
Follow-up	Skin	Scalp	Mucous	Total activity score	Skin	Scalp	Total damage score	Total score
1	10	6	2	18	5	1	6	24
2	15	10	6	31	8	1	9	40
3	25	10	15	50	8	1	9	59
4	25	10	15	50	6	1	7	57
5	18	6	4	28	6	0	6	34
6	5	4	0	9	4	0	4	13

The PDAI has a total possible score ranging 0–263, with 250 points representing disease activity (120 points for skin activity, 10 points for scalp activity and 120 points for mucosal activity). 13 points for total disease damage (12 points for skin damage, 1 point for scalp damage). Extent of Pemphigus according to the PDAI total scores: moderate—0–15 points; significant—15–45 points; extensive—> 45 points